Congenital short bowel syndrome associated with appendiceal agenesis and functional intestinal obstruction

Abstract

Congenital short bowel with functional intestinal obstruction and absence of appendix vermiformis is a very rare condition with poor prognosis. Seventeen cases of congenital short bowel have been reported previously in the literature, The etiology is unknown, In this report, a case of congenital short bowel, combined with functional intestinal obstruction, malrotation, and absence of the appendix vermiformis, is presented and the pathogenesis discussed. Copyright (C) 1998 by W.B. Saunders Company.