Polyarteritis nodosa in patients with Familial Mediterranean fever (FMF): A concomitant disease or a feature of FMF?

Abstract

Background: Familial Mediterranean fever (FMF) is caused by mutations in the gene encoding pyrin and is characterized by self-limited, recurrent attacks of fever and serositis. Vasculitis has been increasingly reported in FMF, A study evaluating the prognosis in FMF and polyarteritis nodosa (PAN) patients has not been reported previously.