Behcet's Syndrome and Nervous System Involvement

Abstract

Although Beh double dagger et's syndrome (BS) is classified as a rare disease in European countries and the USA, its neurologic involvement "neuro-Beh double dagger et's syndrome (NBS)" is commonly included in the differential diagnosis of many inflammatory and vascular central nervous system (CNS) disorders. Clinical and neuroimaging findings support two major forms of NBS: parenchymal NBS (p-NBS) and an extra-parenchymal form that presents with cerebral venous sinus thrombosis (CVST). The present review summarizes recent findings on the etiopathogenesis and clinico-radiological features of this disorder as well as its treatment options.