INFANTILE GENETIC AGRANULOCYTOSIS (KOSTMANN TYPE) - A CASE-REPORT

Abstract

SEVERE PERIODONTITIS IN A PATIENT WITH INFANTILE genetic agranulocytosis (Kostmann syndrome) is presented. This rare syndrome is inherited as an autosomal recessive pattern and characterized by severe neutropenia. The periodontal status and treatment of the patient is described. It is concluded that periodontal therapy including scaling, root planing, soft tissue curettage, and the use of selected antimicrobial agents can be successful in this particular syndrome.