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dc.contributor.authorCigdem, Humeyra
dc.contributor.authorAktuglu-Zeybek, Cigdem
dc.contributor.authorDede, Elif
dc.contributor.authorKIYKIM, Ertuğrul
dc.contributor.authorCANSEVER, Mehmet Şerif
dc.contributor.authorZÜBARİOĞLU, Tanyel
dc.date.accessioned2021-03-02T15:43:56Z
dc.date.available2021-03-02T15:43:56Z
dc.date.issued2021
dc.identifier.citationZÜBARİOĞLU T., Dede E., Cigdem H., KIYKIM E., CANSEVER M. Ş. , Aktuglu-Zeybek C., "Impact of sodium phenylbutyrate treatment in acute management of maple syrup urine disease attacks: a single-center experience", JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM, cilt.34, ss.121-126, 2021
dc.identifier.issn0334-018X
dc.identifier.othervv_1032021
dc.identifier.otherav_b150e6ca-69cd-4831-aeb8-bee01919dafc
dc.identifier.urihttp://hdl.handle.net/20.500.12627/1613
dc.identifier.urihttps://doi.org/10.1515/jpem-2020-0356
dc.description.abstractObjectives: Accurate management of metabolic decompensation in maple syrup urine disease (MSUD) has a crucial role, as acute attacks can cause neurological sequels and can be life threatening. Here, we aimed to evaluate effect of sodium phenylbutyrate (NaPBA) in acute management of MSUD attacks.
dc.language.isoeng
dc.subjectİç Hastalıkları
dc.subjectEndokrinoloji ve Metabolizma Hastalıkları
dc.subjectEndocrinology
dc.subjectEndocrine and Autonomic Systems
dc.subjectPediatrics
dc.subjectPediatrics, Perinatology and Child Health
dc.subjectEndocrinology, Diabetes and Metabolism
dc.subjectLife Sciences
dc.subjectHealth Sciences
dc.subjectSağlık Bilimleri
dc.subjectDahili Tıp Bilimleri
dc.subjectÇocuk Sağlığı ve Hastalıkları
dc.subjectTıp
dc.subjectPEDİATRİ
dc.subjectKlinik Tıp (MED)
dc.subjectKlinik Tıp
dc.subjectENDOKRİNOLOJİ VE METABOLİZMA
dc.titleImpact of sodium phenylbutyrate treatment in acute management of maple syrup urine disease attacks: a single-center experience
dc.typeMakale
dc.relation.journalJOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM
dc.contributor.departmentİstanbul Üniversitesi-Cerrahpaşa , Cerrahpaşa Tıp Fakültesi , Dahili Tıp Bilimleri Bölümü
dc.identifier.volume34
dc.identifier.issue1
dc.identifier.startpage121
dc.identifier.endpage126
dc.contributor.firstauthorID2518925


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