Development and Initial Validation of the Macrophage Activation Syndrome/Primary Hemophagocytic Lymphohistiocytosis Score, a Diagnostic Tool that Differentiates Primary Hemophagocytic Lymphohistiocytosis from Macrophage Activation Syndrome
Yazar
Li, Caifeng
Kitoh, Toshiyuki
Sanner, Helga
Merino, Rosa
Astigarraga, Itziar
Alessio, Maria
Jeng, Michael
Chasnyk, Vyacheslav
Nichols, Kim E.
Zeng Huasong, Zeng Huasong
Kasapcopur, Ozgur
Minoia, Francesca
Bovis, Francesca
Davi, Sergio
Insalaco, Antonella
Lehmberg, Kai
Horne, AnnaCarin
Ravelli, Angelo
Cron, Randy Q.
Martini, Alberto
Ruperto, Nicolino
Micalizzi, Concetta
Shenoi, Susan
Weitzman, Sheila
Espada, Graciela
Gao, Yi-Jin
Anton, Jordi
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Objective To develop and validate a diagnostic score that assists in discriminating primary hemophagocytic lymphohistiocytosis (pHLH) from macrophage activation syndrome (MAS) related to systemic juvenile idiopathic arthritis.
Koleksiyonlar
- Makale [92796]