Complete Labyrinthine Aplasia: Clinical and Radiologic Findings with Review of the Literature

Abstract

BACKGROUND AND PURPOSE: Complete labyrinthine aplasia (CLA), also referred to as Michel aplasia, is a severe congenital anomaly of the inner ear, defined by the complete absence of inner ear structures. The purpose of this study was to document the imaging findings in a series of patients with CLA, with review of the literature, to better understand this anomaly.