Surgical Treatment and Prognosis of Primitive Neuroectodermal Tumors of the Thorax

Abstract

Introduction: Primitive neuroectodermal tumors (PNETs) are rare, rapidly progressive, small-round cell tumors with a poor prognosis despite multimodal therapy, including surgery and chemoradiotherapy. The treatment of choice was unknown since no clinical series with surgical therapy had been reported. We evaluated the impact of multimodal treatment in patients with PNETs located in the thoracic region.